RESUMO
We describe the case of a 52-day-old child who was diagnosed with a rare combination of corrected transposition of great vessels - hypoplastic right ventricle with supracardiac total anomalous pulmonary venous connection.
Assuntos
Veias Pulmonares/anormalidades , Síndrome de Cimitarra/diagnóstico por imagem , Transposição dos Grandes Vasos/diagnóstico por imagem , Cianose/etiologia , Ecocardiografia , Humanos , Imageamento Tridimensional , Lactente , Masculino , Veias Pulmonares/diagnóstico por imagem , Síndrome de Cimitarra/complicações , Tomografia Computadorizada por Raios X , Transposição dos Grandes Vasos/complicaçõesRESUMO
BACKGROUND: Deposition of CPPD crystals occurs in the fibrous and hyaline cartilage of the joints and intervertebral disks of the spine. Half of patients known to have chondrocalcinosis had asymptomatic calcification in the odontoid region. The cases of 12 patients with a spinal cord syndrome secondary to CPPD deposition in the odontoid region were published in the literature. In all those cases, the mass lesion was extradural in location with good outcome after surgical decompression via the transoral route. CASE DESCRIPTION: We report on a rare case of large periodontoid CPPD deposition causing cervicomedullary compression, erosion of the overlying bone, and underlying dura with intradural extension and vertebral artery encasement. CONCLUSIONS: Calcium pyrophosphate dihydrate is a rare cause of cervicomedullary compression. Intradural extension of periodontoid CPPD has not been reported on.